Aortitis and uveitis. A challenging case of Takayasu or Behcet disease?
نویسندگان
چکیده
Methods We presented a challenging case of vasculitis classified considering the EULAR/PRINTO/PRES c-Takayasu Arteritis criteria of 2008 and the International Criteria for Behcet disease of 2013 (ICBD) Results B. is a ten years old boy born in Columbia. At the age of nine, he presented fever that lasted for about 1 month. In the suspect of Kawasaki disease, he was administered Immunoglobulin, without resolution, that persisted until administration of intravenous steroid. His clinical conditions were characterized by asthenia, arthralgia and photophobia. He also presented a heart murmur of 2/6 at centrum cordis. He presented high inflammatory markers, HLA-B51 positivity and proteinuria. Chest radiography, abdomen ultrasound, brain MRI, lumbar puncture and cardiac ultrasound were negative. Instead total body PET and MRI showed inflammation of aortic arch and signs of previous pericarditis. The eye examination showed panuveitis with retinitis. The therapy administered was based on sistemic and ocular steroids and on mycophenolate mofetil with benefit. Table 1.
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